An 11‐year‐old girl presented with a solitary, non‐tender, erythematous, indurated plaque resembling keloid slowly growing on her left upper chest for 5 years (Figure, A). Palpation examination of the lesion showed firm texture and fixity to overlying skin. Histopathology from an elliptical incisional biopsy showed a dermal tumour composed of CD34+ spindle cells arranged in a storiform fascicular pattern extending into the subcutaneous tissue (Figure, B [hematoxylin‐eosin × 40] and C [CD34 stain × 200]), confirming dermatofibrosarcoma protuberans (DFSP). She received Mohs micrographic surgery without recurrence in the 9‐month follow‐up.
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